TY  - JOUR
PY  - 2016//
TI  - Lesch-Nyhan syndrome: disorder of self-mutilating behavior
JO  - International journal of clinical pediatric dentistry
A1  - Jathar, Prasad
A1  - Panse, Amey M.
A1  - Jathar, Madhura
A1  - Gawali, Pritesh N.
SP  - 139
EP  - 142
VL  - 9
IS  - 2
N2  - Lesch-Nyhan syndrome (LNS), a rare inborn error of metabolism, is characterized by self-injurious behavior, which results in partial or total destruction of oral and perioral tissues and/ or fingers. Persistent self-injurious behavior (biting the fingers, hands, lips, and cheeks; banging the head or limbs) is a hallmark of the disease. Prevention of self-mutilation raises significant difficulties. A case of a 10-month-old boy with aggressive behavior and severe lower lip injuries is presented. How to cite this article: Jathar P, Panse AM, Jathar M, Gawali PN. Lesch-Nyhan Syndrome: Disorder of Self-mutilating Behavior. Int J Clin Pediatr Dent 2016;9(2):139-142.<p />  <p>Language: en</p>
LA  - en
SN  - 0974-7052
UR  - http://dx.doi.org/10.5005/jp-journals-10005-1350
ID  - ref1
ER  -