Citation

Sheehy EC, Longhurst P, Pool D, Dandekar M. Int. J. Paediatr. Dent. 1999; 9(4): 299-302.

Affiliation

Department of Orthodontics and Paediatric Dentistry, Guy's Hospital, London, UK. e.sheehy@umds.ac.uk

Copyright

(Copyright © 1999, John Wiley and Sons)

DOI

unavailable

PMID

10815589

Abstract

Hallervorden-Spatz disease (HSD) is a rare neurodegenerative disorder characterized by abnormally high deposits of iron in the brain. This report describes a child with HSD who presented with self-inflicted ulceration of the lip and tongue, which was initiated during periods of intense oro-facial spasms. Other findings included dental caries and trauma to the primary incisors. Comprehensive dental care was carried out under general anaesthesia. The self-mutilation of the oro-facial mucosa was eliminated by placement of upper and lower soft resin bite guards.

Language: en