Citation

Jathar P, Panse AM, Jathar M, Gawali PN. Int. J. Clin. Pediatr. Dent. 2016; 9(2): 139-142.

Affiliation

Postgraduate Student, Department of Pedodontics and Preventive Dentistry, Sinhgad Dental College and Hospital, Pune, Maharashtra, India.

Copyright

(Copyright © 2016, Jaypee Brothers Medical Publishers)

DOI

10.5005/jp-journals-10005-1350

PMID

27365935

PMCID

PMC4921883

Abstract

Lesch-Nyhan syndrome (LNS), a rare inborn error of metabolism, is characterized by self-injurious behavior, which results in partial or total destruction of oral and perioral tissues and/ or fingers. Persistent self-injurious behavior (biting the fingers, hands, lips, and cheeks; banging the head or limbs) is a hallmark of the disease. Prevention of self-mutilation raises significant difficulties. A case of a 10-month-old boy with aggressive behavior and severe lower lip injuries is presented. How to cite this article: Jathar P, Panse AM, Jathar M, Gawali PN. Lesch-Nyhan Syndrome: Disorder of Self-mutilating Behavior. Int J Clin Pediatr Dent 2016;9(2):139-142.

Language: en